Revisão de literatura: Síndrome de Guillain-Barré e Polineuropatia desmielinizante inflamatória crônica / Literature review: Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy
DOI:
https://doi.org/10.34119/bjhrv3n2-115Keywords:
Polineuropatia ¹. diagnóstico diferencial ². Síndrome de Guillain-Barré ³. Polirradiculoneuropatia Desmielinizante Inflamatória Crônica ?.Abstract
Revisão de literatura sobre as Síndromes de Guillain-Barré e Polineuropatia desmielinizante inflamatória crônica. Nesse estudo, os bancos de dados para a pesquisa foram: Scielo, PubMed, MedLine e LILACS. As palavras chaves “Polineuropatia”, “Síndrome de Guillain-Barré” e” Polirradiculoneuropatia Desmielinizante Inflamatória Crônica” foram escolhidas e os artigos selecionados sem definição de datas ou restrição de publicação. Excluindo a duração da evolução, o quadro agudo e formas crônicas são semelhantes em muitos aspectos. Ambos são polirradiculoneuropatias generalizadas, geralmente com citoalbuminologia e dissociação do líquido cefalorraquidiano; ambos nervos exibem anormalidades de condução características de uma neuropatia desmielinizante (redução da velocidade de condução e bloqueio de condução em nervos motores), e patologicamente, ambas mostram inflamação perivenosa multifocal semelhante a infiltrados. Porém, existem diferenças importantes, as mais evidentes são os modos de evolução, respostas ao tratamento e prognóstico. A polineuropatia desmielinizante inflamatória crônica é uma doença comum, embora subdiagnosticada e potencialmente tratável, com prevalência de cerca de 0,5 por 100.000 crianças e 1 a 2 por 100.000 adultos. Semelhanças clínicas com a variante aguda da polineuropatia desmielinizante inflamatória (síndrome de Guillain-Barré) e os efeitos benéficos da imunossupressão terapia sugerem uma patogênese imunomediada. Desde as primeiras descrições de pacientes com polineuropatias crônicas responsivas a corticosteroides por Austin,o espectro da apresentação clínica e do arsenal de diagnóstico aumentaram e outras opções terapêuticas evoluíramReferences
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