Doença de Erdheim-Chester: relato de caso / Erdheim-Chester disease: a case report Erdheim-Chester disease: a case report
DOI:
https://doi.org/10.34119/bjhrv5n1-011Keywords:
Doença de Erdheim-Chester, Xantogranuloma, Imunohistoquímica.Abstract
A doença de Erdheim-Chester é uma rara histiocitose de células não-Langerhans, primeiramente descrita por Jakob Erdheim e William Chester em 1930 de etiologia desconhecida. Clinicamente, pode manifestar sinais e sintomas multiorgânico e o diagnóstico baseia-se em achados radiológicos e anatomopatológicos. Foi relatado um caso da doença onde se estudaram os achados clínicos e radiológicos.
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